The Journal of Bone and Joint Surgery, Vol 64, Issue 1 95-103, Copyright © 1982 by Journal of Bone and Joint Surgery, Inc
Ollier's Disease. An assessment of angular deformity, shortening, and pathological fracture in twenty-one patients
F Shapiro
A retrospective review of twenty-one patients with Ollier's disease showed
that the lesion involved the femur and tibia most frequently, and that
those bones accounted for the large majority of clinical problems. Angular
deformities were common; 80 per cent of the affected femora had clinically
significant varus or valgus angulation in the distal part and 42 per cent
of the affected tibiae had proximal or distal deformity. The apex of the
angulation, when present, was metaphyseal, with the concavity on the side
that was more extensively involved by the enchondromas. Osteotomies were
done frequently to correct angulation; all healed well. Deformity in the
distal part of the femur frequently required repeat osteotomy to achieve a
straight bone at skeletal maturity, The extent of shortening, which always
was present in the involved limb, closely paralleled the extent of
involvement, The discrepancies in limb lengths prior to surgical treatment
averaged 9.8 centimeters (range, 4.3 to 35.7 centimeters). Epiphyseal
arrest, when appropriately timed, was effective in correcting or limiting
the discrepancies, but partial (medial or lateral) epiphyseal arrest to
correct angular deformity was ineffective. Diaphyseal lengthening was done
on six occasions, once in the femur and five times in the tibia and fibula,
with good results. Fourteen pathological fractures occurred in seven of the
twenty-one patients, and all healed uneventfully with conservative
treatment.
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