The Journal of Bone and Joint Surgery, Vol 59, Issue 4 451-460, Copyright © 1977 by Journal of Bone and Joint Surgery, Inc
Management of bleeding and associated complications of hemophilia in the hand and forearm
JE Lancourt, MS Gilbert and MA Posner
Hemorrhage into the hand and forearm in hemophiliacs can be devastating if
not treated early and properly. Of 200 hemophiliacs followed from 1969 to
1976, thirty-four had lesions of the hand and forearm. Hemarthrosis, the
most common musculo-skeletal manifestation of hemophilia, occurred in the
wrist and hand on only ten occasions. Superficial hemorrhage in the seven
cases seen was not followed by significant sequelae. Bleeding into the
anterior muscles and into the volar aspect of the wrist, on the other hand,
was complicated by contracture, neuropathy, or both in six cases. Early
diagnosis, replacement of the missing clotting factor, and immobilization
are essential. Fasciotomy should also be considered, though it was not done
in this series. Once a Volkmann's contracture is established, surgical
reconstruction is required. The fractures in the hemophiliacs in this
series, as in others, healed with normal periosteal callus formation and at
a normal rate. Pseudotumors of the small bones of the hand have been
described but were not seen in this series. Conservative therapy is
suggested. After appropriate hematological evaluation to identify the
missing factor and to exclude the presence of antibodies, it is now
possible to control bleeding while proceeding with the necessary treatment
to restore function and prevent deformity.