Journal of Bone and Joint Surgery, 1974;56:458-465.
© 1974 by The Journal of Bone and Joint Surgery, Inc
Primary Epithelioid Sarcoma of the Hand and Forearm
A REVIEW OF THIRTEEN CASES
RICHARD S. BRYAN M.D.1,
EDWARD H. SOULE M.D.1,
JAMES H. DOBYNS M.D.1,
DOUGLAS J. PRITCHARD M.D.1, and
RONALD L. LINSCHEID M.D.1
1 From the Mayo Clinie and Mayo Foundation, Rochester
Of eighty-five primary soft-tissue and sixteen primary bone sarcomas involving the hand and forearm, thirteen were epithelioid sarcomas, making this lesion third in frequency after fibrosarcoma and rhabdomyosarcoma in the whole series and first in frequency in the hand. In all thirteen patients the initial diagnosis was misleading; and recurrence, metastasis, or both occurred in all but the one patient who had primary forearm amputation. Primary en bloc excision and midforearm amputation are recommended if the lesion recurs.