Vascular Hamartomata and Infantile Angioectatic Osteohyperplasia of the Extremities

A Study of Ninety-Four Cases

¹ Istituto Ortopedico Rizzoli, Clinica Ortopedica della Universitá di Bologna, Bologna

A classification of vascular hamartomata and vascular dysplasias of the extremities occurring in early life is proposed, based on experience with ninety-four cases studlied by a variety of techniques. Six general classifications are made: localized cutaneous and subcutaneous vascular hamartomata, localized deep vascular hamartomata, extensive deep vascular hamartomata, multiple deep vascular hamartomata, diffuse deep vascular hamartomata, and infantile angioectatic osteohyperplasia. The techniques used for the investigation of these lesions include clinical observation, roentgenography, arteriography, phlebography, lymphography, sphygmography, oxygen saturation tests of the blood, histology, and three-dimensional reconstructions of lesions from serial sections. The results of these studies of many of the lesions are reported. Particularly stressed are the characteristics of the different types of such hamartomata, mostly depending on their diffusion and on the size of their communications with the general circulation. Arteriovenous fistulae and venous dysplasia, both congenital, are associated with hamartomata, as evidenced in the six groups under examination.

The sharp difference between diffuse vascular hamartomata and infantile angioectatic osteohyperplasia is pointed out.

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